Trisomy 18 Case, with and without Cardiac Surgery

Herlina Dimiati, Cut Nanda Feby Ayulinda

Abstract


Trisomy 18, known as Edwards Syndrome, is the second-largest chromosomal disorder with a poor prognosis with the survival rate from 5 to 10% at one year of age. The most common factors underlying death are congenital heart defects, heart failure, and pulmonary hypertension. Cardiac surgery performed to patients with Trisomy 18 is associated with a reduction of mortality. This case report presents two cases of Trisomy 18, in which one of them underwent cardiac surgery.


Keywords


trisomy 18; cardiac surgery; mortality

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DOI: https://doi.org/10.33258/birex.v2i3.1163

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